Frataxin (Marker of Friedreich Ataxia) (FXN/2124), 0.2mg/mL

Catalog number BNUB2190-100

Price for BNUB2190-100

Size / count 1x 100 µL

About this product

Frataxin is a nuclear-encoded mitochondrial protein implicated in Friedreich's ataxia (FRDA), a human autosomal recessive neurodegenerative disease. Lack of Frataxin causes iron to accumulate in the mitochondrial matrix suggesting that Frataxin is involved in mitochondrial iron homeostasis and possibly in iron transport. Frataxin has an alpha-beta fold consisting of two helices flanking an antiparallel beta sheet. Primary antibodies are available purified, or with a selection of fluorescent CF® Dyes and other labels. CF® Dyes offer exceptional brightness and photostability. Note: Conjugates of blue fluorescent dyes like CF®405S and CF®405M are not recommended for detecting low abundance targets, because blue dyes have lower fluorescence and can give higher non-specific background than other dye colors.

Specifications

Catalog number: BNUB2190-100
Size / count: 1x 100 µL
Dry ice: No
Hazardous: No
Discontinued: No
CAS Number: 9007-83-4
Synonyms: CyaY; d-FXN; FARR; Frataxin mature form; Frataxin (81-210) ; FRDA; Friedreich ataxia protein; Fxn; i-FXN; m56-FXN; m78-FXN; m81-FXN; X25
UNSPSC: 41116161
UNSPSC Description: Primary and secondary antibodies for multiple methodology immunostaining detection application
Gene Name: FXN
Gene ID: 2395
NCBI Gene ID: 20685
UniProt: Q16595
Swiss Prot: Q16595
Host: Mouse
Species Reactivity: Human
Reactivity: Faxin
Immunogen: Recombinant fragment of human Frataxin (FXN) protein (around aa 57-210) (exact sequence is proprietary)
Target Antigen: Faxin
Clonality: Monoclonal
Clone: FXN/2124
Type: Primary
Source: Animal
Origin: Animal
Applications: IHC, FFPE (verified) |WB (verified)
Positive Control: HepG2, Panc-2, HL-60 or HEK293 cells. Pancreas and Liver.
Stability: 2 years
Concentration: 0.2 mg/mL
Buffer: PBS, 0.05% BSA, 0.05% azide
Molecular Weight: 14 kDa
Shipping Conditions: RT (ND)
Storage Conditions: Stable at room temperature or 37°C (98°F) for 7 days.
Shelf Life: Guaranteed for at least 24 months from date of receipt when stored as recommended
Fragment: IgG2b, kappa
Species: Mus musculus (mouse), BSA from bovine serum (Bos taurus) or recombinant BSA produced in Chinese hamster ovary cells.
Classification: PBS, 0.05% BSA, 0.05% sodium azide (CAS 26628-22-8)
Conjugate: Purified, with BSA

Frequently Asked Questions

What is the catalog number for Frataxin (Marker of Friedreich Ataxia) (FXN/2124), 0.2mg/mL?

The catalog number for Frataxin (Marker of Friedreich Ataxia) (FXN/2124), 0.2mg/mL is BNUB2190-100.

What sizes are available for Frataxin (Marker of Friedreich Ataxia) (FXN/2124), 0.2mg/mL?

Frataxin (Marker of Friedreich Ataxia) (FXN/2124), 0.2mg/mL is available in the following size(s): 1x 100 µL.

Is Frataxin (Marker of Friedreich Ataxia) (FXN/2124), 0.2mg/mL in stock?

Frataxin (Marker of Friedreich Ataxia) (FXN/2124), 0.2mg/mL is currently made to order / not held in immediate stock. Contact us for lead time.

Who manufactures Frataxin (Marker of Friedreich Ataxia) (FXN/2124), 0.2mg/mL?

Frataxin (Marker of Friedreich Ataxia) (FXN/2124), 0.2mg/mL is manufactured by Biotium.

What is the estimated delivery time for Frataxin (Marker of Friedreich Ataxia) (FXN/2124), 0.2mg/mL?

Estimated delivery time for Frataxin (Marker of Friedreich Ataxia) (FXN/2124), 0.2mg/mL is approximately 15 business day(s), depending on your location.

Where can I find the safety data sheet (SDS/MSDS) for Frataxin (Marker of Friedreich Ataxia) (FXN/2124), 0.2mg/mL?

The safety data sheet for Frataxin (Marker of Friedreich Ataxia) (FXN/2124), 0.2mg/mL is available here: https://biotium.com/wp-content/uploads/2018/06/SDS-primary-antibodies.pdf.

What is Frataxin (Marker of Friedreich Ataxia) (FXN/2124), 0.2mg/mL used for?

Can I return this product if I ordered the wrong one?

As a consumer, you have a 14-day right of withdrawal from receipt under EU consumer protection law, submitted via our withdrawal/cancellation request form. Note this applies to unused, undamaged products, and doesn’t override the expiry/storage conditions on performance-based claims.

Is this product tested for endotoxin levels?

Endotoxin testing status is noted on the datasheet where applicable, particularly for recombinant proteins intended for cell-based or functional assays. If this isn’t listed and you need confirmation, contact support with the catalogue number.

Can I request additional validation data, such as western blot images, for this product?

Additional data may be available on request. Contact our technical support team with the catalogue number and we’ll check what supporting documentation the supplier can provide.