HMBS Recombinant Rabbit Monoclonal Antibody [SC65-07] — image 1 of 2

Product details

HMBS Recombinant Rabbit Monoclonal Antibody [SC65-07]

Catalog number ET1610-91

Price for ET1610-91

Size / count 100 µL

About this product

PBGD (porphobilinogen deaminase), also designated hydroxymethylbilane synthase, is a cytoplasmic enzyme found in the heme synthesis pathway. PBGD belongs to the HMBS (hydroxymethylbilane synthase) family. Deficiency of PBGD causes errors in pyrrole metabolism, which in turn leads to an inherited autosomal disorder called acute intermittent porphyria (AIP). AIP is characterized by acute attacks of neurological dysfunctions with hypertension, tachycardia, peripheral neurologic disturbances, abdominal pain and excessive amounts of aminolevulinic acid and porphobilinogen in the urine.

Specifications

Catalog number: ET1610-91
Size / count: 100 µL
Dry ice: No
Hazardous: No
Discontinued: No
CAS Number: 9000-83-3
Product Name Alternative: HEM3_HUMAN antibody HMBS antibody Hydroxymethylbilane synthase antibody PBG D antibody PBG-D antibody PBGD antibody PORC antibody Porphobilinogen deaminase antibody porphyria, acute; Chester type antibody Pre uroporphyrinogen synthase antibody Pre-uroporphyrinogen synthase antibody UPS antibody Uroporphyrinogen I synthase antibody Uroporphyrinogen I synthetase antibody
Abbreviation: PBG-D, HMBS
Swiss Prot: P08397 Human, P22907 Mouse, P19356 Rat
Cellular Locus: Cytoplasm.
Host: Rabbit
Species Reactivity: Human, Mouse, Rat
Immunogen: Recombinant protein within Human HMBS aa 1-132 / 299.
Isotype: IgG
Conjugation: Non-conjugated
Type: Recombinant Rabbit monoclonal Antibody
Applications: WB
Positive Control: Hela cell lysate, 293T cell lysate, K562 cell lysates.
Concentration: 1 mg/mL
Dilution: WB: 1:500
Purity: Protein A affinity purified.
Form: Liquid
Buffer: 1*TBS (pH7.4), 0.05% BSA, 40% Glycerol. Preservative: 0.05% Sodium Azide.
Molecular Weight: Predicted band size: 39 kDa
Storage Conditions: Store at +4°C after thawing. Aliquot store at -20°C or -80°C. Avoid repeated freeze / thaw cycles.
Recombinant Antibody: Yes

Frequently Asked Questions

What is the catalog number for HMBS Recombinant Rabbit Monoclonal Antibody [SC65-07]?

The catalog number for HMBS Recombinant Rabbit Monoclonal Antibody [SC65-07] is ET1610-91.

What sizes are available for HMBS Recombinant Rabbit Monoclonal Antibody [SC65-07]?

HMBS Recombinant Rabbit Monoclonal Antibody [SC65-07] is available in the following size(s): 100 µL.

Is HMBS Recombinant Rabbit Monoclonal Antibody [SC65-07] in stock?

HMBS Recombinant Rabbit Monoclonal Antibody [SC65-07] is currently made to order / not held in immediate stock. Contact us for lead time.

What is HMBS Recombinant Rabbit Monoclonal Antibody [SC65-07] used for?

Is there an additional fee for hazardous or dry ice shipping of this product?

Yes, if this product requires dry ice or is classed as hazardous for transport, the additional fee will be explicitly shown in your quotation before you confirm the order, so there are no surprise charges later.

How many freeze-thaw cycles can this product tolerate?

We recommend aliquoting the product upon receipt to avoid repeated freeze-thaw cycles, which can reduce activity and stability. This is your responsibility once the product has been delivered.

Is antigen retrieval required for IHC with this antibody?

Recommended antigen retrieval methods, where applicable, are listed on the datasheet under the IHC protocol section.